|
Link to this page
Your search term(s) "cystic disease" returned 9 results.
Displaying all search results.
Kidney Dysplasia. Bethesda, MD: National Kidney and Urologic Diseases Information Clearinghouse. 2008. 6 p.
This fact sheet describes kidney dysplasia, a condition in which the internal structures of one or both of a baby’s kidneys do not develop normally. Fluid-filled sacs called cysts replace normal kidney tissue. Kidney dysplasia usually happens in only one kidney. A baby with one working kidney can grow normally and has few, if any, health problems. Babies with kidney dysplasia affecting both kidneys generally do not survive pregnancy. Those who do survive need dialysis and a kidney transplant very early in life. Written in a question-and-answer format, the fact sheet explains how kidney dysplasia happens, the causes of kidney dysplasia, the signs or complications of kidney dysplasia, how kidney dysplasia is diagnosed, treatment strategies, and the long-term outlook for a child with kidney dysplasia. The fact sheet includes a list of questions for parents to ask their health care provider about the child’s kidney dysplasia and related problems. The author notes that kidney dysplasia may have genetic causes and is often part of several genetic syndromes that affect other body systems. Children and adults with only one working kidney should have regular checkups for high blood pressure and kidney damage. A final section of the fact sheet briefly notes the importance of ongoing research studies. The fact sheet includes contact information for four resource organizations and concludes with a brief description of the goals and activities of the National Kidney and Urologic Diseases Information Clearinghouse. 3 figures.
Full Record Printer Friendly Version
Medullary Sponge Kidney. Bethesda, MD: National Kidney and Urologic Diseases Information Clearinghouse. 2008. 6 p.
This fact sheet describes medullary sponge kidney (MSK), a birth defect of the tubules inside the kidneys. In a normal kidney, urine flows through these tubules as it is being formed. In MSK, tiny sacs called cysts form in the medulla, the inner part of the kidney, creating a spongelike appearance. The cysts keep urine from flowing freely through the tubules. Written in a question-and-answer format, the fact sheet explains how the kidneys function and discusses the signs and symptoms of MSK, how MSK is diagnosed, and treatment strategies. Although MSK is present at birth, most cases do not appear to be inherited. Problems caused by MSK include hematuria, or blood in the urine; kidney stones; and urinary tract infections (UTIs). However, these problems do not usually appear until the person is in his or her 30s or 40s. Diagnosis of MSK may require a type of x ray called an intravenous pyelogram. Once the condition is diagnosed, treatment focuses on curing UTIs, removing kidney stones, and preventing recurrent infections and stones. A final section of the fact sheet briefly notes the importance of ongoing research studies. The fact sheet includes contact information for four resource organizations: the American Association of Kidney Patients at 1–800–749–2257 or www.aakp.org, the American Kidney Fund at 1–800–638–8299 or www.kidneyfund.org, the Life Options Rehabilitation Resource Center at 1–800–468–7777 or www.lifeoptions.org, and the National Kidney Foundation at 1–800–622–9010 or www.kidney.org. The fact sheet concludes with a brief description of the goals and activities of the National Kidney and Urologic Diseases Information Clearinghouse. 3 figures.
Full Record Printer Friendly Version
Congenital Abnormalities of the Kidney and Urinary Tract. IN: Hogg, R., ed. Kidney Disorders in Children and Adolescents: A Global Perspective of Clinical Practice. New York, NY: Informa Healthcare USA. 2006. pp 35-52.
This chapter about congenital abnormalities of the kidney and urinary tract is from a textbook that presents a global perspective of clinical practice regarding kidney disorders in children and adolescents. The author stresses that congenital abnormalities of the urinary tract are an important cause of morbidity and, occasionally, mortality in children. Topics covered include development of the renal tract, antenatally detected urinary tract abnormalities (AUTAs), antenatal intervention, investigations, renal agenesis, renal fusion and ectopia, duplex systems, renal dysplasia and hypoplasia, multicystic dysplastic kidney, pelviureteric junction (PUJ) obstruction, vesicoureteric junction (VUJ) obstruction, vesicoureteral reflux (VUR), posterior urethral valves (PUV), neuropathic bladder, renal cystic disease, familial nephronophthisis and medullary cystic disease complex, autosomal dominant medullary cystic kidney disease, medullary sponge kidney, and tuberous sclerosis complex (TSC). The author concludes that the use of antenatal ultrasound has resulted in increasing numbers of asymptomatic infants being referred for postnatal investigations and has changed perceptions of the natural history of many conditions. Pediatricians and nephrologists will have an increasing role to play in the ongoing monitoring process of children with these congenital conditions. The chapter includes black-and-white illustrations and photographs and concludes with an extensive list of references. 16 figures. 2 tables. 26 references.
Full Record Printer Friendly Version
Cystic Diseases of the Kidney. IN: Kellogg Parsons, J.; James Wright, E., eds. Brady Urology Manual. New York, NY: Informa Healthcare USA. 2006. pp 107-114.
This chapter about cystic diseases of the kidney is from a reference handbook that offers a comprehensive overview of urology, presented in outline and bulleted formats for ease of access in the busy health care world of hospital emergency rooms and outpatient clinics. The author notes that simple renal cyst is a common, benign condition that is usually detected incidentally. The chapter covers general information, presentation, diagnosis, and treatment of simple renal cyst, acquired renal cystic disease, autosomal dominant polycystic kidney disease (ADPKD), and autosomal recessive polycystic kidney disease (ARPKD). The Bosniak classification system is recommended to distinguish simple cysts from complex renal cysts and cystic renal cell carcinoma (RCC). Acquired renal cystic disease occurs in patients with kidney failure and is characterized by bilateral cortical and/or medullary cysts. ADPKD is an inherited disease of the collecting duct characterized by multiple large renal cysts, progressive renal insufficiency, and extrarenal manifestations, including hepatic cysts and cerebral artery aneurysm. Treatment for ADPKD and ARPKD is supportive care. The chapter concludes with a list of references for additional reading. 19 references.
Full Record Printer Friendly Version
PKD Patient's Manual: Understanding and Living with Autosomal Dominant Polycystic Kidney Disease. Kansas City, MO: Polycystic Kidney Disease Foundation. 2006. 33 p.
This booklet provides information about autosomal dominant polycystic kidney disease (ADPKD) to those who have the disease, those who are at risk due to an affected family member, and people who care about someone who has been diagnosed with ADPKD. The primary manifestation of ADPKD is cysts in the kidney, cysts as well as other abnormalities can occur in other areas of the body. Written in a question-and-answer format, this booklet covers the epidemiology of ADPKD, symptoms, genetics and inheritance, the ADPKD genes, screening tests for ADPKD, kidney anatomy and function, cysts and their impact on the kidney, high blood pressure (hypertension), weight loss, exercise, sodium, potassium, tobacco use, acute and chronic pain in ADPKD, blood in the urine, urinary tract infection (UTI), kidney stones, liver cysts, dialysis and transplantation, mitral valve prolapse, intracranial aneurysms, hernias, diverticula, pregnancy, diet therapy, fluids, caffeine, children with ADPKD, symptoms of kidney failure, and common tests that are done to diagnose and monitor cystic disease. The booklet concludes with a list of resource organizations through which readers can get more information. 12 figures. 1 table. 2 references.
Full Record Printer Friendly Version
Multicystic Dysplastic Kidney: Conservative Management and Follow-Up. Renal Failure. 27(2): 189-192. 2005.
This article reports on the authors’ experience in the conservative management of patients with multicystic dysplastic kidney (MCDK) disease. The authors describe the care of 35 children, 18 male and 17 female, who were diagnosed with MCDK between 1992 and 2003 and followed at the Riyadh Armed Forces Hospital. The authors performed static scintigraphy with dimercaptosuccinic acid and micturating cystourethrogram in all patients; ultrasound was performed every 3 months, then annually. Mean age at diagnosis during the postnatal period was 2.4 days. Follow-up ultrasound examinations showed partial involution in 17 patients (48.6 percent) and complete involution in 13 (37.1 percent); 5 (14.3 percent) showed an unchanged size without any pathological manifestations. The mean age at complete or partial involution of the lesion was 43.7 months. No child developed complications such as hypertension or tumors, and all maintained normal growth and development. The authors conclude that MCDK lesions are often benign, and the affected kidneys tend to show involution with time. 2 figures. 2 tables. 26 references.
Full Record Printer Friendly Version
Options for Patients with Kidney Failure. IN: Danovitch, G.M. Handbook of Kidney Transplantation. Philadelphia, PA: Lippincott Williams and Wilkins. 2005. pp. 1-22.
This chapter, from a handbook that offers a practical guide for health care providers who manage kidney transplant patients, outlines the current treatment options for patients with kidney failure. The authors stress that for most patients with kidney failure, kidney transplantation has the greatest potential for restoring a healthy, productive life. However, virtually all transplant recipients have been exposed, at least to some extent, to the adverse consequences of chronic kidney disease (CKD). This must be taken into consideration when planning for renal replacement therapy. The authors review the stages of CKD, demographics of the end-stage renal disease (ESRD) population, hemodialysis, peritoneal dialysis, long-term complications of dialysis (anemia, renal osteodystrophy, uremic neuropathy, amyloidosis, acquired cystic disease, cancer of the kidney and urinary tract, dialysis access failure), transplantation considerations including patient survival, and choosing an appropriate renal replacement therapy. 6 figures. 3 tables. 16 references.
Full Record Printer Friendly Version
Medullary Cystic Kidney Disease Type 1 in a Large Native-American Kindred. American Journal of Kidney Diseases. 44(4): 611-617. October 2004.
Autosomal dominant medullary cystic kidney disease type 1 (MCKD1) is a hereditary tubulointerstitial renal disease. This article reports on the difficulties of establishing the diagnosis of MCKD in a large Native American kindred solely by means of clinical criteria. The authors report on a study of 50 individuals from a large Native American family in North Carolina with apparent autosomal dominant nephropathy (kidney disease). Haplotype (genetic) analysis for 34 individuals was performed. The results in this kindred show a wider range of age of disease onset than previously reported. Gout and hypertension were common, but no patient reported symptoms of salt wasting. The authors found that establishing a diagnosis of MCKD solely on clinical findings is difficult because signs and symptoms may be subtle, renal cysts may be absent in more than 50 percent of affected individuals, and renal histological abnormalities are nonspecific. In patients presenting with renal insufficiency from apparent interstitial disease, a thorough family history and genetic linkage studies are required to establish a diagnosis of MCKD. The authors conclude that MCKD is underdiagnosed and the true incidence of MCKD1 in the general population may be underestimated. No further living-related transplantation should be performed until genetic testing can exclude potentially affected donors. 2 figures. 3 tables. 20 references.
Full Record Printer Friendly Version
Natural History of Multicystic Kidney Conservatively Managed: A Prospective Study. Pediatric Nephrology. 19(10): 1102-1107. October 2004.
This article reports on a study of the long-term clinical results of conservative management of children with unilateral multicystic dysplastic kidneys (MCDK). Between 1989 and 2002, 43 children with MCDK detected by prenatal ultrasonography were prospectively followed. Follow-up ultrasound (US) examinations were performed at 6-month intervals during the first 2 years of life and yearly thereafter. The mean follow-up time was 42 months (range 12 to 156 months). Two children developed hypertension (high blood pressure) during follow-up. US scans demonstrated partial involution of the MCDK in 30 cases (70 percent) and complete involution in 8 cases (19 percent). The absolute MCDK length remained almost unchanged in 5 children (11 percent). A total of 33 (76.7 percent) contralateral kidneys underwent compensatory hypertrophy (the uninvolved kidneys grew larger to compensate for the kidney damaged by MCDK), reaching a renal length above the 95th percentile during follow-up. The authors conclude that the natural history of MCDK is usually benign but patients must have long-term follow-up with US scans and blood pressure measurements. 3 figures. 1 table. 35 references.
Full Record Printer Friendly Version
Displaying all search results.
Start a new search.
|
